Kartagener 综合征伴弥漫性泛细支气管炎1例
linical and pathological features of Kartagener syndrom complicated with diffuse pan bronchiolitis
目的 探讨Kartagener 综合征合并弥漫性泛细支气管炎(DPB)的临床特征。方法 回顾分析1例Kartagener 综合征合并弥漫性泛细支气管炎的临床表现、影像特点和实验室检查,并复习相关文献。结果 Kartagener综合征是一种罕见的遗传性疾病,它的特点是支气管扩张症、副鼻窦炎以及内脏转位。弥漫性泛细支气管炎(DPB)也是一种少见病。它的病理特点为终末细支气管和呼吸性细支气管管壁增厚,慢性炎细胞浸润。结论 Kartagener综合征合并弥漫性泛细支气管炎值得引起临床注意,临床表现及影像特点有助于诊断,最终确诊依赖病理。
Objective:To explore the clinical characteristics of Kartagener syndrome complicated with diffuse pan bronchiolitis(DPB). Methods To analyze retrospectively the clinical manifestations, imaging features and laboratory examination of one case with Kartagener syndrome complicated with DPB, and review related literature. Results Kartagener syndrome is a rare inherited disease characterized by visceral inversion, bronchiectasis, and chronic nasal sinusitis. Diffuse pan bronchiolitis is also a rare disease. It’s histopathological examination showed thickening of the walls of the terminal bronchioles and respiratory bronchioles with infiltration of inflammatory cells. Conclusions Kartagener syndrome complicated with DPB has certain clinical and imaging features. Pathological examination is necessary for the final diagnosis.
阚海峰、林勇
临床医学内科学基础医学
Kartagener 综合征弥漫性泛细支气管炎支气管扩张副鼻窦炎
Kartagener syndromeiffuse pan bronchiolitisBronchiectasisccessory sinusitis
阚海峰,林勇.Kartagener 综合征伴弥漫性泛细支气管炎1例[EB/OL].(2009-08-27)[2025-08-02].http://www.paper.edu.cn/releasepaper/content/200908-455.点此复制
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